Sjögren Reticular Dystrophy is an autosomal recessive condition characterized by a bilateral and symmetrical hyperpigmented reticular pattern of pigment epithelial clumping at the level of the retinal pigment epithelium, with pigment epithelial hyperplastic and atrophic degenerative areas that often look like a fishnet. It starts centrally and spreads to the periphery.
The patients are usually asymptomatic and they have good vision.
In the early phases, fluorescein angiography shows the typical fundus, with polygonal units of hyperfluorescence and dark patches of hypofluorescence from areas of hyperpigmentation.
