{"id":74753,"date":"2021-11-23T15:29:43","date_gmt":"2021-11-23T15:29:43","guid":{"rendered":"https:\/\/www.atlasrleye.com\/cecite-nocturne-congenitale-stationnaire\/"},"modified":"2025-07-15T13:04:07","modified_gmt":"2025-07-15T13:04:07","slug":"cecite-nocturne-congenitale-stationnaire","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/fr\/cecite-nocturne-congenitale-stationnaire\/","title":{"rendered":"C\u00c9CIT\u00c9 NOCTURNE CONG\u00c9NITALE STATIONNAIRE"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb]<div class=\"ult-spacer spacer-6a03e5a3a90f4\" data-id=\"6a03e5a3a90f4\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">La maladie d\u2019Oguchi est une maladie autosomique r\u00e9cessive caract\u00e9ris\u00e9e par c\u00e9cit\u00e9 nocturne stationnaire cong\u00e9nitale et par le ph\u00e9nom\u00e8ne de Mizuo-Nakamura depuis la naissance ou la petite enfance, avec une vision diurne normal.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">La r\u00e9tine pr\u00e9sente une d\u00e9coloration jaune-dor\u00e9 ou blanc-argent\u00e9 du fond de l&rsquo;\u0153il en pr\u00e9sence de lumi\u00e8re qui dispara\u00eet apr\u00e8s l&rsquo; adaptation \u00e0 l&rsquo;obscurit\u00e9 et qui r\u00e9appara\u00eet \u00e0 nouveau \u00e0 la lumi\u00e8re. On pense que ce ph\u00e9nom\u00e8ne peut \u00eatre provoqu\u00e9 par une stimulation excessive des b\u00e2tonnets.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le fond de l\u2019\u0153il ne montre pas des alt\u00e9rations maculaires ou atrophie chorior\u00e9tinienne, ni de preuve de spicules. L\u2019acuit\u00e9 visuelle et le calibre des vaisseaux de la r\u00e9tine sont normaux et la r\u00e9ponse de c\u00f4nes \u00e0 l&rsquo;\u00e9lectror\u00e9tinogramme est normale.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le diagnostic est bas\u00e9 sur de signes cliniques, la fondoscopie et l\u2019\u00e9lectror\u00e9tinographie, et est confirm\u00e9 par des tests g\u00e9n\u00e9tiques.<\/p>\n<p style=\"font-size: 16px;\">Diagnostic Diff\u00e9rentiel:<\/p>\n<ul>\n<li style=\"font-size: 16px;\">R\u00e9tinopathie pigmentaire li\u00e9e \u00e0 l\u2019X<\/li>\n<li style=\"font-size: 16px;\">Dystrophie des c\u00f4nes et b\u00e2tonnets \u00e0 d\u00e9but pr\u00e9coce<\/li>\n<li style=\"font-size: 16px;\">Dystrophie progressive des c\u00f4nes<\/li>\n<\/ul>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_images_carousel images=\u00a0\u00bb20468,20467&Prime; img_size=\u00a0\u00bbmedium\u00a0\u00bb speed=\u00a0\u00bb2000&Prime; autoplay=\u00a0\u00bbyes\u00a0\u00bb hide_pagination_control=\u00a0\u00bbyes\u00a0\u00bb wrap=\u00a0\u00bbyes\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1752583865853{margin-bottom: 10px !important;}\u00a0\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-5676\"><div id=\"counter_4980661086a03e5a3a935e\" data-id=\"counter_4980661086a03e5a3a935e\"  data-ultimate-target='#counter-responsv-wrap-5676 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"1\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_4980661086a03e5a3a935e\"  data-ultimate-target='#counter-responsv-wrap-5676 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Cas Cliniques<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00a0\u00bb.vc_custom_1752583891393{margin-bottom: 10px !important;}\u00a0\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Cas Cliniques<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752583938812{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/fr\/cecite-nocturne-congenitale-stationnaire\/cas-clinique-1\/\">Cas Clinique 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb20467,20138&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752584492866{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4658\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4658 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3743\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3743 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">8<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4599\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4599 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text] La maladie d\u2019Oguchi est une maladie autosomique r\u00e9cessive caract\u00e9ris\u00e9e par c\u00e9cit\u00e9 nocturne stationnaire cong\u00e9nitale et [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74753","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74753","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/comments?post=74753"}],"version-history":[{"count":8,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74753\/revisions"}],"predecessor-version":[{"id":118175,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74753\/revisions\/118175"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/media?parent=74753"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}