{"id":74649,"date":"2021-11-23T15:49:24","date_gmt":"2021-11-23T15:49:24","guid":{"rendered":"https:\/\/www.atlasrleye.com\/degenerescence-vitreoretinienne-hereditaire\/"},"modified":"2025-07-15T01:42:59","modified_gmt":"2025-07-15T01:42:59","slug":"degenerescence-vitreoretinienne-hereditaire","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/fr\/degenerescence-vitreoretinienne-hereditaire\/","title":{"rendered":"D\u00c9G\u00c9N\u00c9RESCENCE VITR\u00c9OR\u00c9TINIENNE H\u00c9R\u00c9DITAIRE"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231635506431773-0d8d0743-1f0b|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb]<div class=\"ult-spacer spacer-6a04d597a77ea\" data-id=\"6a04d597a77ea\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">Trois des plus \u00e9minents d\u00e9g\u00e9n\u00e9rescences vitr\u00e9or\u00e9tiniennes h\u00e9r\u00e9ditaires sont le syndrome de Stickler, le syndrome de Wagner et le syndrome de Goldman-Favr\u00e9.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le syndrome de Stickler est caract\u00e9ris\u00e9 par l\u2019association des signes oculaires de d\u00e9collement de r\u00e9tine et myopie avec arthropathie progressive transmise selon un mode autosomique dominant. Les caract\u00e9ristiques oculaires du syndrome de Stickler, \u00e0 l&rsquo;exception de la cataracte corticale pr\u00e9coce, comprennent myopie \u00e9lev\u00e9e, d\u00e9g\u00e9n\u00e9rescence vitr\u00e9enne, r\u00e9tinopathie pigmentaire, atrophie chor\u00efor\u00e9tinienne et des d\u00e9chirures de r\u00e9tine.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le syndrome de Wagner pr\u00e9sente seulement signes oculaires: caract\u00e9ristiques de la myopie, d\u00e9g\u00e9n\u00e9rescence vitr\u00e9enne, pigmentation perivascularaire, rev\u00eatement des vaisseaux p\u00e9riph\u00e9riques, d\u00e9g\u00e9n\u00e9rescence et amincissement de la r\u00e9tine, et atrophie chor\u00efor\u00e9tinienne.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le syndrome de Goldman-Favr\u00e9 est une d\u00e9g\u00e9n\u00e9rescence autosomique r\u00e9cessive caract\u00e9ris\u00e9e par nyctalopie, perte progressive de la vision centrale et p\u00e9riph\u00e9rique, cataracte progressive, r\u00e9tinopathie pigmentaire, r\u00e9tinoschisis maculaire et p\u00e9riph\u00e9rique, et d\u00e9g\u00e9n\u00e9rescence vitr\u00e9enne.<\/p>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_images_carousel images=\u00a0\u00bb20526,20521,20582,20601,20640,20639&Prime; img_size=\u00a0\u00bbmedium\u00a0\u00bb speed=\u00a0\u00bb2000&Prime; autoplay=\u00a0\u00bbyes\u00a0\u00bb hide_pagination_control=\u00a0\u00bbyes\u00a0\u00bb wrap=\u00a0\u00bbyes\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1752543318240{margin-bottom: 10px !important;}\u00a0\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-4470\"><div id=\"counter_5367582126a04d597a7a2f\" data-id=\"counter_5367582126a04d597a7a2f\"  data-ultimate-target='#counter-responsv-wrap-4470 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"3\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_5367582126a04d597a7a2f\"  data-ultimate-target='#counter-responsv-wrap-4470 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Cas Cliniques<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00a0\u00bb.vc_custom_1752543337587{margin-bottom: 10px !important;}\u00a0\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Cas Cliniques<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752543433030{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/fr\/degenerescence-vitreoretinienne-hereditaire\/cas-clinique-1\/\">Cas Clinique 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb20526,20521&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752543449120{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9089\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9089 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">4<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9060\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9060 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">41<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-2683\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-2683 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752543398689{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/fr\/degenerescence-vitreoretinienne-hereditaire\/cas-clinique-2\/\">Cas Clinique 2<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb20582,20601&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752543462821{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6886\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6886 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">3<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3137\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3137 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">57<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-2723\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-2723 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752543417020{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/fr\/degenerescence-vitreoretinienne-hereditaire\/cas-clinique-3\/\">Cas Clinique 3<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb20640,20639&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752543474492{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6564\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6564 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6365\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6365 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">17<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-8468\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-8468 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231635506431773-0d8d0743-1f0b|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text] Trois des plus \u00e9minents d\u00e9g\u00e9n\u00e9rescences vitr\u00e9or\u00e9tiniennes h\u00e9r\u00e9ditaires sont le syndrome de Stickler, le syndrome de [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74649","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74649","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/comments?post=74649"}],"version-history":[{"count":39,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74649\/revisions"}],"predecessor-version":[{"id":118110,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74649\/revisions\/118110"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/media?parent=74649"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}