{"id":74285,"date":"2021-11-23T16:25:26","date_gmt":"2021-11-23T16:25:26","guid":{"rendered":"https:\/\/www.atlasrleye.com\/fundus-albipunctatus\/"},"modified":"2025-07-15T10:57:27","modified_gmt":"2025-07-15T10:57:27","slug":"fundus-albipunctatus","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/fr\/fundus-albipunctatus\/","title":{"rendered":"FUNDUS ALBIPUNCTATUS"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb]<div class=\"ult-spacer spacer-69e1003866d88\" data-id=\"69e1003866d88\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">Le fundus albipunctatus est une dystrophie r\u00e9tinienne rare, de transmission autosomique r\u00e9cessive, caus\u00e9e par des mutations dans le g\u00e8ne RDH5, responsable par l\u2019enzyme microsomale de l\u2019\u00e9pithelium pigmentaire de la r\u00e9tine (EPR) impliqu\u00e9 dans la transduction des photor\u00e9cepteurs. Elle se manifeste dans la premi\u00e8re d\u00e9cennie de vie avec nyctalopie et difficult\u00e9 de l\u2019adaptation \u00e0 l\u2019obscurit\u00e9 apr\u00e8s une exposition \u00e0 la lumi\u00e8re intense. L\u2019acuit\u00e9 visuelle et la vision de couleurs sont bonnes, bien que pas tout \u00e0 fait normal.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le fond montre des taches jaune-blanches, situ\u00e9es \u00e0 la mi-p\u00e9riph\u00e9rie de la r\u00e9tine, \u00e9pargnant la macula. Ces l\u00e9sions sont situ\u00e9es au niveau de l&rsquo; EPR et ont tendance \u00e0 augmenter en nombre et en pro\u00e9minence avec l&rsquo;\u00e2ge. Sont bilat\u00e9rales et sym\u00e9triques.<\/p>\n<p style=\"font-size: 16px;\">Diagnostic Diff\u00e9rentiel:<\/p>\n<ul>\n<li style=\"font-size: 16px;\">Flecks b\u00e9nignes de la r\u00e9tine<\/li>\n<li style=\"font-size: 16px;\">Variantes Bothnia et Newfoundland<\/li>\n<li style=\"font-size: 16px;\">Retinitis punctata albescens<\/li>\n<li style=\"font-size: 16px;\">R\u00e9tinopathie de Kandori<\/li>\n<\/ul>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_images_carousel images=\u00a0\u00bb21095,21094&Prime; img_size=\u00a0\u00bbmedium\u00a0\u00bb speed=\u00a0\u00bb2000&Prime; autoplay=\u00a0\u00bbyes\u00a0\u00bb hide_pagination_control=\u00a0\u00bbyes\u00a0\u00bb wrap=\u00a0\u00bbyes\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1752576864970{margin-bottom: 10px !important;}\u00a0\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-6159\"><div id=\"counter_250432217269e100386701a\" data-id=\"counter_250432217269e100386701a\"  data-ultimate-target='#counter-responsv-wrap-6159 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"1\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_250432217269e100386701a\"  data-ultimate-target='#counter-responsv-wrap-6159 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Cas Cliniques<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00a0\u00bb.vc_custom_1752576873640{margin-bottom: 10px !important;}\u00a0\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Cas Cliniques<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752576903560{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a title=\"Cas Clinique 1\" href=\"https:\/\/www.atlasrleye.com\/fr\/fundus-albipunctatus\/cas-clinique-1\/\">Cas Clinique 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb21094,21095&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752576896159{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4480\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4480 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9445\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9445 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">5<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6536\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6536 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text] Le fundus albipunctatus est une dystrophie r\u00e9tinienne rare, de transmission autosomique r\u00e9cessive, caus\u00e9e par des [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74285","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74285","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/comments?post=74285"}],"version-history":[{"count":8,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74285\/revisions"}],"predecessor-version":[{"id":118128,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74285\/revisions\/118128"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/media?parent=74285"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}