{"id":74270,"date":"2022-01-28T11:43:02","date_gmt":"2022-01-28T11:43:02","guid":{"rendered":"https:\/\/www.atlasrleye.com\/manifestations-oculaires-de-lhomocystinurie\/cas-clinique-1\/"},"modified":"2024-03-20T12:41:46","modified_gmt":"2024-03-20T12:41:46","slug":"cas-clinique-1","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/fr\/manifestations-oculaires-de-lhomocystinurie\/cas-clinique-1\/","title":{"rendered":"Cas clinique 1"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; add_icon=\u00a0\u00bbtrue\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading text=\u00a0\u00bbManifestations oculaires de l\u2019homocystinurie &#8211; Cas clinique 1&Prime; font_container=\u00a0\u00bbtag:h1|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fmanifestations-oculaires-de-lhomocystinurie%2F|title:MANIFESTATIONS%20OCULAIRES%20DE%20L%E2%80%99HOMOCYSTINURIE|\u00a0\u00bb]<div class=\"ult-spacer spacer-6a1083d21583d\" data-id=\"6a1083d21583d\" data-height=\"70\" data-height-mobile=\"70\" data-height-tab=\"70\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column]<div class=\"ult-spacer spacer-6a1083d2158bf\" data-id=\"6a1083d2158bf\" data-height=\"10\" data-height-mobile=\"10\" data-height-tab=\"10\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div><div class=\"ult-spacer spacer-6a1083d215919\" data-id=\"6a1083d215919\" data-height=\"20\" data-height-mobile=\"20\" data-height-tab=\"20\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row gap=\u00a0\u00bb35&Prime; equal_height=\u00a0\u00bbyes\u00a0\u00bb][vc_column width=\u00a0\u00bb1\/2&Prime;][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<p style=\"font-size: 18px; text-align: justify;\"><span style=\"color: #000000;\"><img loading=\"lazy\" decoding=\"async\" class=\" wp-image-21099 alignleft\" src=\"https:\/\/www.atlasrleye.com\/wp-content\/uploads\/2022\/01\/o01-ti02-128701-20091130-029-300x253.jpg\" alt=\"\" width=\"210\" height=\"177\">R\u00e9tinographie chez un patient \u00e2g\u00e9 de 3 ans atteint d&rsquo;Homocystinurie et d&rsquo;Acid\u00e9mie M\u00e9thylmalonique. Hypopigmentation g\u00e9n\u00e9ralis\u00e9e du fond d\u2019\u0153il. Maculopathie secondaire \u00e0 l&rsquo;atrophie centrale de l&rsquo;\u00e9pith\u00e9lium pigmentaire de la r\u00e9tine et d\u00e9g\u00e9n\u00e9rescence des photor\u00e9cepteurs \u00e9voluant vers un pseudo-colobome.<\/span><\/p>\n<p>[\/vc_column_text][\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00a0\u00bb1\/2&Prime;][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<p style=\"text-align: justify; font-size: 18px;\"><span style=\"color: #000000;\"><img loading=\"lazy\" decoding=\"async\" class=\" wp-image-21100 alignleft\" src=\"https:\/\/www.atlasrleye.com\/wp-content\/uploads\/2022\/01\/o02-ti07-128701-20091130-096-300x253.jpg\" alt=\"\" width=\"215\" height=\"181\">Angiographie \u00e0 la fluoresc\u00e9ine en phase tardive montrant une maculopathie en cible, dans le m\u00eame cas.<\/span><\/p>\n<p>[\/vc_column_text][\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text]<\/p>\n<h3><span style=\"color: #5f1b52;\">\u00c9valuations<br \/>\n<\/span><\/h3>\n<p>[\/vc_column_text][vc_tta_accordion active_section=\u00a0\u00bb99&Prime; no_fill=\u00a0\u00bbtrue\u00a0\u00bb collapsible_all=\u00a0\u00bbtrue\u00a0\u00bb][vc_tta_section i_icon_fontawesome=\u00a0\u00bbfar fa-calendar-alt\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb title=\u00a0\u00bb1\u00e8re \u00c9valuation &#8211; 30 11 2009&Prime; tab_id=\u00a0\u00bb1643201210935-53e8de92-3b06&Prime;][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Angiographie \u00e0 la Fluoresc\u00e9ine<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb68176,68164,68161,68158,68173,68179,68155&Prime; img_size=\u00a0\u00bb251&#215;250&Prime;][\/vc_column_inner][\/vc_row_inner][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">R\u00e9tinographie Couleur<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb68170,68167&Prime; img_size=\u00a0\u00bb251&#215;250&Prime;][\/vc_column_inner][\/vc_row_inner][\/vc_tta_section][vc_tta_section i_icon_fontawesome=\u00a0\u00bbfar fa-calendar-alt\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb title=\u00a0\u00bb2\u00e8me \u00c9valuation &#8211; 22 10 2012&Prime; tab_id=\u00a0\u00bb1643370329620-5b732628-5bbd\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/2&Prime;][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Autofluorescence<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb68191,68182&Prime; img_size=\u00a0\u00bb251&#215;250&Prime;][\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/2&Prime;][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">R\u00e9tinographie Couleur<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb68185,68188&Prime; img_size=\u00a0\u00bb251&#215;206&Prime;][\/vc_column_inner][\/vc_row_inner][\/vc_tta_section][vc_tta_section i_icon_fontawesome=\u00a0\u00bbfar fa-calendar-alt\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb title=\u00a0\u00bb3\u00e8me \u00c9valuation &#8211; 21 04 2023&Prime; tab_id=\u00a0\u00bb1710937460697-95fbfc3d-df35&Prime;][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/2&Prime;][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Autofluorescence<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb105325,105329&Prime; img_size=\u00a0\u00bb251&#215;206&Prime;][\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/2&Prime;][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Infrarouge<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb105308,105312&Prime; img_size=\u00a0\u00bb193&#215;206&Prime;][\/vc_column_inner][\/vc_row_inner][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">OCT (B-Scan) longitudinal<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb105336,105343,105347,105303&Prime; img_size=\u00a0\u00bb420*110&Prime;][\/vc_column_inner][\/vc_row_inner][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">R\u00e9tinographie Couleur<\/p>\n<div style=\"text-indent: 20px;\">\n<p style=\"font-size: 14px; text-align: justify;\"><span style=\"color: #000000;\">AV: 20\/200. Nystagmus horizontal. Fond d\u2019\u0153il avec alterations pigmentaires et pseudocolobome maculaire atrophique centromaculaire. Changements de l\u2019EPR p\u00e9riph\u00e9rique typiques de la maladie.<\/span><\/p>\n<\/div>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb105316,105321&Prime; img_size=\u00a0\u00bb251&#215;206&Prime; css=\u00a0\u00bb.vc_custom_1710938213298{margin-top: -30px !important;}\u00a0\u00bb][\/vc_column_inner][\/vc_row_inner][\/vc_tta_section][\/vc_tta_accordion][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; add_icon=\u00a0\u00bbtrue\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading text=\u00a0\u00bbManifestations oculaires de l\u2019homocystinurie &#8211; Cas clinique 1&Prime; font_container=\u00a0\u00bbtag:h1|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fmanifestations-oculaires-de-lhomocystinurie%2F|title:MANIFESTATIONS%20OCULAIRES%20DE%20L%E2%80%99HOMOCYSTINURIE|\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column][\/vc_column][\/vc_row][vc_row gap=\u00a0\u00bb35&Prime; equal_height=\u00a0\u00bbyes\u00a0\u00bb][vc_column width=\u00a0\u00bb1\/2&Prime;][vc_row_inner][vc_column_inner][vc_column_text] R\u00e9tinographie chez un patient \u00e2g\u00e9 [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":74259,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74270","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74270","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/comments?post=74270"}],"version-history":[{"count":13,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74270\/revisions"}],"predecessor-version":[{"id":105669,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74270\/revisions\/105669"}],"up":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74259"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/media?parent=74270"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}