{"id":74023,"date":"2021-11-23T16:45:26","date_gmt":"2021-11-23T16:45:26","guid":{"rendered":"https:\/\/www.atlasrleye.com\/syndrome-dusher\/"},"modified":"2025-07-15T00:03:51","modified_gmt":"2025-07-15T00:03:51","slug":"syndrome-dusher","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/fr\/syndrome-dusher\/","title":{"rendered":"SYNDROME D\u2019USHER"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb]<div class=\"ult-spacer spacer-69f278ce31a2a\" data-id=\"69f278ce31a2a\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">Le syndrome d\u2019Usher est caract\u00e9ris\u00e9 par l&rsquo;association d&rsquo;une r\u00e9tinopathie pigmentaire avec perte d\u2019audition cong\u00e9nitale neurosensorielle partielle ou profonde. Elle est class\u00e9e en 4 types:<\/p>\n<ul>\n<li style=\"font-size: 16px;\">Type I &#8211; surdit\u00e9 cong\u00e9nitale avec r\u00e9tinopathie pigmentaire pr\u00e9coce<\/li>\n<li style=\"font-size: 16px;\">Type II &#8211; surdit\u00e9 partiel cong\u00e9nitale et d\u00e9but tardif de r\u00e9tinopathie pigmentaire<\/li>\n<li style=\"font-size: 16px;\">Type III &#8211; audition normale et vision au d\u00e9but qui s&rsquo;aggravent avec l&rsquo;\u00e2ge; psychose<\/li>\n<li style=\"font-size: 16px;\">Type IV &#8211; li\u00e9e \u00e0 l&rsquo;X avec r\u00e9tinopathie pigmentaire, cataracte, surdit\u00e9, ataxie et retard mentale<\/li>\n<\/ul>\n<p style=\"text-align: justify; font-size: 16px;\">Les sympt\u00f4mes oculaires comprennent la photophobie, nyctalopie, probl\u00e8mes d&rsquo;adaptation \u00e0 l\u2019obscurit\u00e9, dyschromatopsie, photopsies et diminution des champs visuels.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Au fond oculaire sont observ\u00e9s agglom\u00e9r\u00e9s \u00e0 la p\u00e9riph\u00e9rie et dans les zones veineuses (\u00e9perons osseux). Peut \u00e9galement se produire une att\u00e9nuation des vaisseaux r\u00e9tiniens, p\u00e2leur de la papille optique, \u0153d\u00e8me maculaire cysto\u00efde et cellules pigment\u00e9es dans le vitr\u00e9.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Le diagnostic des diff\u00e9rents types de syndrome d&rsquo;Usher, peut \u00eatre confirm\u00e9 par des essais mol\u00e9culaires.<\/p>\n<p style=\"font-size: 16px;\">Diagnostic diff\u00e9rentiel<\/p>\n<ul>\n<li style=\"font-size: 16px;\">Hypertrophie cong\u00e9nitale de l&rsquo;\u00e9pith\u00e9lium pigmentaire de la r\u00e9tine<\/li>\n<li style=\"font-size: 16px;\">C\u00e9cit\u00e9 nocturne cong\u00e9nitale stationnaire<\/li>\n<li style=\"font-size: 16px;\">D\u00e9ficience en vitamine A<\/li>\n<\/ul>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_images_carousel images=\u00a0\u00bb21760,21759,21758,21757&Prime; img_size=\u00a0\u00bbmedium\u00a0\u00bb speed=\u00a0\u00bb2000&Prime; autoplay=\u00a0\u00bbyes\u00a0\u00bb hide_pagination_control=\u00a0\u00bbyes\u00a0\u00bb wrap=\u00a0\u00bbyes\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1752537505084{margin-bottom: 10px !important;}\u00a0\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-7512\"><div id=\"counter_87229932669f278ce31c05\" data-id=\"counter_87229932669f278ce31c05\"  data-ultimate-target='#counter-responsv-wrap-7512 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"2\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_87229932669f278ce31c05\"  data-ultimate-target='#counter-responsv-wrap-7512 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Cas Cliniques<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00a0\u00bb.vc_custom_1752537514742{margin-bottom: 10px !important;}\u00a0\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Cas Cliniques<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752537536661{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a title=\"Cas Clinique 1\" href=\"https:\/\/www.atlasrleye.com\/fr\/syndrome-dusher\/cas-clinique-1\/\">Cas Clinique 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb21759,21758&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752537546782{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3897\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3897 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-1021\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-1021 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">21<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3900\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3900 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00a0\u00bb1\/4&Prime;][vc_column_text css=\u00a0\u00bb.vc_custom_1752537740536{margin-bottom: 0px !important;}\u00a0\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a title=\"Cas Clinique 2\" href=\"https:\/\/www.atlasrleye.com\/fr\/syndrome-dusher\/cas-clinique-2\/\">Cas Clinique 2<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00a0\u00bbimage_grid\u00a0\u00bb images=\u00a0\u00bb21757,21760&Prime; img_size=\u00a0\u00bb150&Prime; css=\u00a0\u00bb.vc_custom_1752537728503{margin-bottom: 10px !important;margin-left: -20px !important;}\u00a0\u00bb][vc_row_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-8932\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-8932 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6314\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6314 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">20<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00a0\u00bb1\/5&Prime; offset=\u00a0\u00bbvc_col-xs-1\/5&Prime;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4578\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4578 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00a0\u00bbSYNDROMES ET DYSTROPHIES R\u00c9TINIENNES\u00a0\u00bb font_container=\u00a0\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Ffr%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00a0\u00bb][vc_text_separator title=\u00a0\u00bb\u00a0\u00bb i_icon_fontawesome=\u00a0\u00bbfas fa-eye\u00a0\u00bb i_color=\u00a0\u00bbcustom\u00a0\u00bb i_size=\u00a0\u00bblg\u00a0\u00bb color=\u00a0\u00bbcustom\u00a0\u00bb border_width=\u00a0\u00bb8&Prime; css=\u00a0\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00a0\u00bb add_icon=\u00a0\u00bbtrue\u00a0\u00bb accent_color=\u00a0\u00bb#bababa\u00a0\u00bb i_custom_color=\u00a0\u00bb#bababa\u00a0\u00bb][vc_custom_heading source=\u00a0\u00bbpost_title\u00a0\u00bb font_container=\u00a0\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&Prime; use_theme_fonts=\u00a0\u00bbyes\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb3\/4&Prime;][vc_column_text] Le syndrome d\u2019Usher est caract\u00e9ris\u00e9 par l&rsquo;association d&rsquo;une r\u00e9tinopathie pigmentaire avec perte d\u2019audition cong\u00e9nitale neurosensorielle [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74023","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74023","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/comments?post=74023"}],"version-history":[{"count":10,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74023\/revisions"}],"predecessor-version":[{"id":118077,"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/pages\/74023\/revisions\/118077"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/fr\/wp-json\/wp\/v2\/media?parent=74023"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}