{"id":74757,"date":"2021-11-23T15:29:43","date_gmt":"2021-11-23T15:29:43","guid":{"rendered":"https:\/\/www.atlasrleye.com\/ceguera-nocturna-estacionaria-congenita\/"},"modified":"2025-07-15T13:05:27","modified_gmt":"2025-07-15T13:05:27","slug":"ceguera-nocturna-estacionaria-congenita","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/es\/ceguera-nocturna-estacionaria-congenita\/","title":{"rendered":"CEGUERA NOCTURNA ESTACIONARIA CONG\u00c9NITA"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00bbS\u00cdNDROMES Y DISTROFIAS RETINIANAS\u00bb font_container=\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=\u00bbyes\u00bb link=\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Fes%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00bb][vc_text_separator title=\u00bb\u00bb i_icon_fontawesome=\u00bbfas fa-eye\u00bb i_color=\u00bbcustom\u00bb i_size=\u00bblg\u00bb color=\u00bbcustom\u00bb border_width=\u00bb8&#8243; css=\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00bb add_icon=\u00bbtrue\u00bb accent_color=\u00bb#bababa\u00bb i_custom_color=\u00bb#bababa\u00bb][vc_custom_heading source=\u00bbpost_title\u00bb font_container=\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=\u00bbyes\u00bb]<div class=\"ult-spacer spacer-6a03dc0b48af8\" data-id=\"6a03dc0b48af8\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb3\/4&#8243;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">La enfermedad de Oguchi es una enfermedad autos\u00f3mica recesiva caracterizada por ceguera nocturna estacionaria cong\u00e9nita y por lo fen\u00f3meno de Mizuo-Nakamura desde el nacimiento o la primera infancia, con visi\u00f3n de d\u00eda normal.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">La retina tiene una t\u00edpica descoloraci\u00f3n difusa amarilla-dorada o gris-plateada del fondo de ojo en la presencia de la luz, que desaparece despu\u00e9s de la adaptaci\u00f3n a la oscuridad y aparece de nuevo tras la exposici\u00f3n a la luz. Se cree que este fen\u00f3meno puede ser causado por la sobreestimulaci\u00f3n de los bastones.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">No se observan alteraciones maculares o atrofia retinocoroidea y no hay evidencia de esp\u00edculas. La agudeza visual y el calibre de los vasos de la retina son normales y la respuesta de los conos en el electrorretinograma es normal.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">El diagn\u00f3stico se basa en los hallazgos cl\u00ednicos, fundoscop\u00eda y electrorretinografia y es confirmado por los testes gen\u00e9ticos.<\/p>\n<p style=\"font-size: 16px;\">Diagn\u00f3stico Diferencial:<\/p>\n<ul>\n<li style=\"font-size: 16px;\">Retinosis pigmentaria ligado a X<\/li>\n<li style=\"font-size: 16px;\">Distrofia de conos y bastones de in\u00edcio precoz<\/li>\n<li style=\"font-size: 16px;\">Distrofia de conos progressiva<\/li>\n<\/ul>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00bb1\/4&#8243;][vc_images_carousel images=\u00bb20468,20467&#8243; img_size=\u00bbmedium\u00bb speed=\u00bb2000&#8243; autoplay=\u00bbyes\u00bb hide_pagination_control=\u00bbyes\u00bb wrap=\u00bbyes\u00bb css=\u00bb.vc_custom_1752583865853{margin-bottom: 10px !important;}\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-9373\"><div id=\"counter_9131079846a03dc0b48c74\" data-id=\"counter_9131079846a03dc0b48c74\"  data-ultimate-target='#counter-responsv-wrap-9373 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"1\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_9131079846a03dc0b48c74\"  data-ultimate-target='#counter-responsv-wrap-9373 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Casos Cl\u00ednicos<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00bb.vc_custom_1752583891393{margin-bottom: 10px !important;}\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Casos Cl\u00ednicos<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb1\/4&#8243;][vc_column_text css=\u00bb.vc_custom_1752583938812{margin-bottom: 0px !important;}\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/es\/ceguera-nocturna-estacionaria-congenita\/caso-clinico-1\/\">Caso Cl\u00ednico 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00bbimage_grid\u00bb images=\u00bb20467,20138&#8243; img_size=\u00bb150&#8243; css=\u00bb.vc_custom_1752584492866{margin-bottom: 10px !important;margin-left: -20px !important;}\u00bb][vc_row_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4842\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4842 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-8428\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-8428 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">8<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9475\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9475 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00bbS\u00cdNDROMES Y DISTROFIAS RETINIANAS\u00bb font_container=\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=\u00bbyes\u00bb link=\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Fes%2Fatlas%2F%231636632807269-1444524b-3ed4|\u00bb][vc_text_separator title=\u00bb\u00bb i_icon_fontawesome=\u00bbfas fa-eye\u00bb i_color=\u00bbcustom\u00bb i_size=\u00bblg\u00bb color=\u00bbcustom\u00bb border_width=\u00bb8&#8243; css=\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00bb add_icon=\u00bbtrue\u00bb accent_color=\u00bb#bababa\u00bb i_custom_color=\u00bb#bababa\u00bb][vc_custom_heading source=\u00bbpost_title\u00bb font_container=\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=\u00bbyes\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb3\/4&#8243;][vc_column_text] La enfermedad de Oguchi es una enfermedad autos\u00f3mica recesiva caracterizada por ceguera nocturna estacionaria cong\u00e9nita [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74757","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/74757","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/comments?post=74757"}],"version-history":[{"count":11,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/74757\/revisions"}],"predecessor-version":[{"id":118176,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/74757\/revisions\/118176"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/media?parent=74757"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}