{"id":71768,"date":"2021-11-17T16:49:54","date_gmt":"2021-11-17T16:49:54","guid":{"rendered":"https:\/\/www.atlasrleye.com\/retinoschisis-juvenil-ligado-a-x\/"},"modified":"2025-09-11T23:06:54","modified_gmt":"2025-09-11T23:06:54","slug":"retinoschisis-juvenil-ligado-a-x","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/es\/retinoschisis-juvenil-ligado-a-x\/","title":{"rendered":"RETINOSCHISIS JUVENIL LIGADO A X"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=\u00bbENFERMEDADES CONG\u00c9NITAS Y PEDI\u00c1TRICAS DE LA RETINA\u00bb font_container=\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=\u00bbyes\u00bb link=\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Fes%2Fatlas%2F%231635506431773-0d8d0743-1f0b|\u00bb][vc_text_separator title=\u00bb\u00bb i_icon_fontawesome=\u00bbfas fa-eye\u00bb i_color=\u00bbcustom\u00bb i_size=\u00bblg\u00bb color=\u00bbcustom\u00bb border_width=\u00bb8&#8243; css=\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00bb add_icon=\u00bbtrue\u00bb accent_color=\u00bb#bababa\u00bb i_custom_color=\u00bb#bababa\u00bb][vc_custom_heading source=\u00bbpost_title\u00bb font_container=\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=\u00bbyes\u00bb]<div class=\"ult-spacer spacer-6a03dc125af28\" data-id=\"6a03dc125af28\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb3\/4&#8243;][vc_column_text css=\u00bb\u00bb]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">La retinosquisis ligada a X es una enfermedad, bilateral en el 80% de los casos, que ocurre en varones y cl\u00e1sicamente muestra una maculopat\u00eda estrellada y dehiscencias perif\u00e9ricas en la capa de fibras nerviosas. Aparece en la primera d\u00e9cada de la vida o puede estar al nacimiento.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Esta enfermedad est\u00e1 mapeada en el gen XRLS1\/retinoschisin, que codifica las prote\u00ednas necesarias para la adhesi\u00f3n celular.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">El OCT muestra alteraciones del tipo microc\u00edstico de la macula. Las complicaciones en edades m\u00e1s avanzadas y con riesgo para la visi\u00f3n, son el desprendimiento de retina y las hemorragias en el v\u00edtreo.<\/p>\n<p style=\"font-size: 16px;\">Diagn\u00f3stico Diferencial:<\/p>\n<ul>\n<li style=\"font-size: 16px;\">Vitreorretinopatia exudativa familiar<\/li>\n<li style=\"font-size: 16px;\">Enfermedad de Goldman-Favr\u00e9<\/li>\n<li style=\"font-size: 16px;\">Enfermedad de Norrie<\/li>\n<li style=\"font-size: 16px;\">Retinosis pigmentaria<\/li>\n<li style=\"font-size: 16px;\">Retinopat\u00eda de la prematuridad<\/li>\n<li style=\"font-size: 16px;\">S\u00edndrome de Stickler<\/li>\n<\/ul>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00bb1\/4&#8243;][vc_images_carousel images=\u00bb4766,4793,4826,4836,4841,4843&#8243; img_size=\u00bbmedium\u00bb speed=\u00bb2000&#8243; autoplay=\u00bbyes\u00bb hide_pagination_control=\u00bbyes\u00bb wrap=\u00bbyes\u00bb css=\u00bb.vc_custom_1748471769645{margin-bottom: 10px !important;}\u00bb]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-2642\"><div id=\"counter_30966721716a03dc125b089\" data-id=\"counter_30966721716a03dc125b089\"  data-ultimate-target='#counter-responsv-wrap-2642 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"3\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_30966721716a03dc125b089\"  data-ultimate-target='#counter-responsv-wrap-2642 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Casos Cl\u00ednicos<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=\u00bb.vc_custom_1748470290501{margin-bottom: 10px !important;}\u00bb]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Casos Cl\u00ednicos<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb1\/4&#8243;][vc_column_text css=\u00bb.vc_custom_1748470303810{margin-bottom: 0px !important;}\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/es\/retinoschisis-juvenil-ligado-a-x\/caso-clinico-1\/\">Caso Cl\u00ednico 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00bbimage_grid\u00bb images=\u00bb4752,4755&#8243; img_size=\u00bb150&#8243; css=\u00bb.vc_custom_1748470517043{margin-bottom: 10px !important;margin-left: -20px !important;}\u00bb][vc_row_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-5870\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-5870 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">7<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-2729\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-2729 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">86<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3249\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3249 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00bb1\/4&#8243;][vc_column_text css=\u00bb.vc_custom_1748470650944{margin-bottom: 0px !important;}\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/es\/retinoschisis-juvenil-ligado-a-x\/caso-clinico-2\/\">Caso Cl\u00ednico 2<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00bbimage_grid\u00bb images=\u00bb4754,4836&#8243; img_size=\u00bb150&#8243; css=\u00bb.vc_custom_1748470664158{margin-bottom: 10px !important;margin-left: -20px !important;}\u00bb][vc_row_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-7395\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-7395 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9555\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9555 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">17<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9858\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9858 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00bb1\/4&#8243;][vc_column_text css=\u00bb.vc_custom_1748470683095{margin-bottom: 0px !important;}\u00bb]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/es\/retinoschisis-juvenil-ligado-a-x\/caso-clinico-3\/\">Caso Cl\u00ednico 3<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=\u00bbimage_grid\u00bb images=\u00bb5499,5500&#8243; img_size=\u00bb150&#8243; css=\u00bb.vc_custom_1748470761417{margin-bottom: 10px !important;margin-left: -20px !important;}\u00bb][vc_row_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-1397\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-1397 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">3<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-5127\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-5127 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">15<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=\u00bb1\/5&#8243; offset=\u00bbvc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-5073\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-5073 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=\u00bb1\/4&#8243;][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=\u00bbENFERMEDADES CONG\u00c9NITAS Y PEDI\u00c1TRICAS DE LA RETINA\u00bb font_container=\u00bbtag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=\u00bbyes\u00bb link=\u00bburl:https%3A%2F%2Fwww.atlasrleye.com%2Fes%2Fatlas%2F%231635506431773-0d8d0743-1f0b|\u00bb][vc_text_separator title=\u00bb\u00bb i_icon_fontawesome=\u00bbfas fa-eye\u00bb i_color=\u00bbcustom\u00bb i_size=\u00bblg\u00bb color=\u00bbcustom\u00bb border_width=\u00bb8&#8243; css=\u00bb.vc_custom_1637080776101{margin-bottom: -5px !important;}\u00bb add_icon=\u00bbtrue\u00bb accent_color=\u00bb#bababa\u00bb i_custom_color=\u00bb#bababa\u00bb][vc_custom_heading source=\u00bbpost_title\u00bb font_container=\u00bbtag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=\u00bbyes\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00bb3\/4&#8243;][vc_column_text css=\u00bb\u00bb] La retinosquisis ligada a X es una enfermedad, bilateral en el [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-71768","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/71768","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/comments?post=71768"}],"version-history":[{"count":26,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/71768\/revisions"}],"predecessor-version":[{"id":119202,"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/pages\/71768\/revisions\/119202"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/es\/wp-json\/wp\/v2\/media?parent=71768"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}