{"id":74645,"date":"2021-11-23T15:49:24","date_gmt":"2021-11-23T15:49:24","guid":{"rendered":"https:\/\/www.atlasrleye.com\/hereditary-vitreoretinal-degenerations\/"},"modified":"2025-07-15T01:42:29","modified_gmt":"2025-07-15T01:42:29","slug":"hereditary-vitreoretinal-degenerations","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/en\/hereditary-vitreoretinal-degenerations\/","title":{"rendered":"HEREDITARY VITREORETINAL DEGENERATIONS"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231635506431773-0d8d0743-1f0b|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; add_icon=&#8221;true&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading source=&#8221;post_title&#8221; font_container=&#8221;tag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221;]<div class=\"ult-spacer spacer-6a151450c68a2\" data-id=\"6a151450c68a2\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;3\/4&#8243;][vc_column_text]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">Three of the most prominent of the hereditary vitreoretinal degenerations are: Stickler syndrome, Wagner syndrome, and Goldmann-Favr\u00e9 syndrome.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Stickler syndrome is characterized by the association of the ocular findings of retinal detachment and myopia with progressive arthropathy inherited as an autosomal dominant trait. The ocular features of Stickler syndrome, with the exception of early cortical cataract, are primarily posterior segment findings. These include high myopia, vitreous degeneration, pigmentary retinopathy, chorioretinal atrophy, retinal breaks and detachment.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Wagner syndrome describes a condition limited to the eye, with features of myopia, vitreous degeneration, perivascular pigmentation, peripheral vessel sheathing, retinal degeneration and thinning, and atrophy of the choriocapillaris.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Goldmann-Favr\u00e9 syndrome is an autosomal recessive vitreoretinal degeneration characterized by nyctalopia, progressive loss of central and peripheral vision, progressive cataract, pigmentary retinophathy, macular and peripheral retinoschisis, and vitreous degeneration.<\/p>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=&#8221;1\/4&#8243;][vc_images_carousel images=&#8221;20526,20521,20582,20601,20640,20639&#8243; img_size=&#8221;medium&#8221; speed=&#8221;2000&#8243; autoplay=&#8221;yes&#8221; hide_pagination_control=&#8221;yes&#8221; wrap=&#8221;yes&#8221; css=&#8221;.vc_custom_1752543318240{margin-bottom: 10px !important;}&#8221;]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-6631\"><div id=\"counter_36922317006a151450c6c7f\" data-id=\"counter_36922317006a151450c6c7f\"  data-ultimate-target='#counter-responsv-wrap-6631 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"3\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_36922317006a151450c6c7f\"  data-ultimate-target='#counter-responsv-wrap-6631 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Clinical Cases<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=&#8221;.vc_custom_1752543337587{margin-bottom: 10px !important;}&#8221;]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Clinical Cases<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;1\/4&#8243;][vc_column_text css=&#8221;.vc_custom_1752543433030{margin-bottom: 0px !important;}&#8221;]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/en\/hereditary-vitreoretinal-degenerations\/clinical-case-1\/\">Clinical Case 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;20526,20521&#8243; img_size=&#8221;150&#8243; css=&#8221;.vc_custom_1752543449120{margin-bottom: 10px !important;margin-left: -20px !important;}&#8221;][vc_row_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-2867\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-2867 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">4<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4049\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4049 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">41<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-1557\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-1557 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=&#8221;1\/4&#8243;][vc_column_text css=&#8221;.vc_custom_1752543398689{margin-bottom: 0px !important;}&#8221;]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/en\/hereditary-vitreoretinal-degenerations\/clinical-case-2\/\">Clinical Case 2<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;20582,20601&#8243; img_size=&#8221;150&#8243; css=&#8221;.vc_custom_1752543462821{margin-bottom: 10px !important;margin-left: -20px !important;}&#8221;][vc_row_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4102\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4102 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">3<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-9659\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-9659 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">57<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4075\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4075 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=&#8221;1\/4&#8243;][vc_column_text css=&#8221;.vc_custom_1752543417020{margin-bottom: 0px !important;}&#8221;]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/en\/hereditary-vitreoretinal-degenerations\/clinical-case-3\/\">Clinical Case 3<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;20640,20639&#8243; img_size=&#8221;150&#8243; css=&#8221;.vc_custom_1752543474492{margin-bottom: 10px !important;margin-left: -20px !important;}&#8221;][vc_row_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-4894\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-4894 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-8164\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-8164 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">17<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-8900\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-8900 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231635506431773-0d8d0743-1f0b|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; add_icon=&#8221;true&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading source=&#8221;post_title&#8221; font_container=&#8221;tag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221;][\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;3\/4&#8243;][vc_column_text] Three of the most prominent of the hereditary vitreoretinal degenerations are: Stickler syndrome, Wagner syndrome, [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74645","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74645","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/comments?post=74645"}],"version-history":[{"count":45,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74645\/revisions"}],"predecessor-version":[{"id":118109,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74645\/revisions\/118109"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/media?parent=74645"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}