{"id":74251,"date":"2022-01-28T12:25:22","date_gmt":"2022-01-28T12:25:22","guid":{"rendered":"https:\/\/www.atlasrleye.com\/ocular-manifestations-of-neuronal-ceroid-lipofuscinosis\/clinical-case-1\/"},"modified":"2023-05-05T11:09:44","modified_gmt":"2023-05-05T11:09:44","slug":"clinical-case-1","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/en\/ocular-manifestations-of-neuronal-ceroid-lipofuscinosis\/clinical-case-1\/","title":{"rendered":"Clinical Case 1"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231636632807269-1444524b-3ed4|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; add_icon=&#8221;true&#8221; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading text=&#8221;Ocular Manifestations Neuronal Ceroid Lipofuscinosis &#8211; Clinical Case 1&#8243; font_container=&#8221;tag:h1|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Focular-manifestations-of-neuronal-ceroid-lipofuscinosis%2F|title:Ocular%20Manifestations%20Neuronal%20Ceroid%20Lipofuscinosis|&#8221;]<div class=\"ult-spacer spacer-6a03d16e8bc01\" data-id=\"6a03d16e8bc01\" data-height=\"70\" data-height-mobile=\"70\" data-height-tab=\"70\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column]<div class=\"ult-spacer spacer-6a03d16e8bca8\" data-id=\"6a03d16e8bca8\" data-height=\"10\" data-height-mobile=\"10\" data-height-tab=\"10\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div><div class=\"ult-spacer spacer-6a03d16e8bd29\" data-id=\"6a03d16e8bd29\" data-height=\"20\" data-height-mobile=\"20\" data-height-tab=\"20\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row gap=&#8221;35&#8243; equal_height=&#8221;yes&#8221;][vc_column width=&#8221;1\/2&#8243;][vc_row_inner][vc_column_inner width=&#8221;1\/2&#8243;][vc_single_image image=&#8221;69994&#8243; img_size=&#8221;medium&#8221; alignment=&#8221;center&#8221; onclick=&#8221;link_image&#8221;][\/vc_column_inner][vc_column_inner width=&#8221;1\/2&#8243;][vc_column_text]<\/p>\n<p style=\"font-size: 18px; text-align: justify;\"><span style=\"color: #000000;\">Fundus photograph of a 9-year-old female with Neuronal Ceroid Lipofuscinosis (Batten Disease). Note the pale optic disc, very thin vessels, widespread RPE changes and beatten bronze macula.<\/span><\/p>\n<p>[\/vc_column_text][\/vc_column_inner][\/vc_row_inner][\/vc_column][vc_column width=&#8221;1\/2&#8243;][vc_row_inner][vc_column_inner width=&#8221;1\/2&#8243;][vc_single_image image=&#8221;69991&#8243; img_size=&#8221;medium&#8221; alignment=&#8221;center&#8221; onclick=&#8221;link_image&#8221;][\/vc_column_inner][vc_column_inner width=&#8221;1\/2&#8243;][vc_column_text]<\/p>\n<p style=\"text-align: justify; font-size: 18px;\"><span style=\"color: #000000;\">Ultra-widefield photograph in same case, showing the paleness of retina, the character of the avascular peripheral retina and some pigmented deposits on the extreme periphery.<\/span><\/p>\n<p>[\/vc_column_text][\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text]<\/p>\n<h3><span style=\"color: #5f1b52;\">Evaluations<br \/>\n<\/span><\/h3>\n<p>[\/vc_column_text][vc_tta_accordion active_section=&#8221;99&#8243; no_fill=&#8221;true&#8221; collapsible_all=&#8221;true&#8221;][vc_tta_section i_icon_fontawesome=&#8221;far fa-calendar-alt&#8221; add_icon=&#8221;true&#8221; title=&#8221;1st Evaluation &#8211; 17 11 2010&#8243; tab_id=&#8221;1643201210935-53e8de92-3b06&#8243;][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Autofluorescence<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;68199,68196&#8243; img_size=&#8221;193&#215;206&#8243;][\/vc_column_inner][\/vc_row_inner][vc_row_inner][vc_column_inner][vc_column_text]<\/p>\n<div class=\"row py-1\">\n<div class=\"col-12 border-bottom border-gray-light\">\n<p style=\"font-size: 18px;\">Colour retinography<\/p>\n<\/div>\n<\/div>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;68202,68205,68193,68208&#8243; img_size=&#8221;251&#215;206&#8243;][\/vc_column_inner][\/vc_row_inner][\/vc_tta_section][\/vc_tta_accordion][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231636632807269-1444524b-3ed4|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; add_icon=&#8221;true&#8221; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading text=&#8221;Ocular Manifestations Neuronal Ceroid Lipofuscinosis &#8211; Clinical Case 1&#8243; font_container=&#8221;tag:h1|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Focular-manifestations-of-neuronal-ceroid-lipofuscinosis%2F|title:Ocular%20Manifestations%20Neuronal%20Ceroid%20Lipofuscinosis|&#8221;][\/vc_column][\/vc_row][vc_row][vc_column][\/vc_column][\/vc_row][vc_row gap=&#8221;35&#8243; equal_height=&#8221;yes&#8221;][vc_column width=&#8221;1\/2&#8243;][vc_row_inner][vc_column_inner width=&#8221;1\/2&#8243;][vc_single_image image=&#8221;69994&#8243; img_size=&#8221;medium&#8221; alignment=&#8221;center&#8221; [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":74239,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-74251","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74251","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/comments?post=74251"}],"version-history":[{"count":10,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74251\/revisions"}],"predecessor-version":[{"id":81385,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74251\/revisions\/81385"}],"up":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/74239"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/media?parent=74251"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}