{"id":113600,"date":"2024-11-11T12:57:28","date_gmt":"2024-11-11T12:57:28","guid":{"rendered":"https:\/\/www.atlasrleye.com\/?page_id=113600"},"modified":"2025-07-15T13:08:45","modified_gmt":"2025-07-15T13:08:45","slug":"pigmented-paravenous-retinochoroidal-atrophy","status":"publish","type":"page","link":"https:\/\/www.atlasrleye.com\/en\/pigmented-paravenous-retinochoroidal-atrophy\/","title":{"rendered":"Pigmented Paravenous Retinochoroidal Atrophy"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231636632807269-1444524b-3ed4|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; add_icon=&#8221;true&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading source=&#8221;post_title&#8221; font_container=&#8221;tag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221;]<div class=\"ult-spacer spacer-6a03c7a22d4c7\" data-id=\"6a03c7a22d4c7\" data-height=\"30\" data-height-mobile=\"0\" data-height-tab=\"\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"\" style=\"clear:both;display:block;\"><\/div>[\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;3\/4&#8243;][vc_column_text css=&#8221;&#8221;]<\/p>\n<div class=\"w-100 middle-subtext text-justify hidden-text\">\n<p style=\"text-align: justify; font-size: 16px;\">Pigmented Paravenous Retinochoroidal Atrophy (PPRCA) is a rare disorder of unknown etiology, characterized by perivenous pigment accumulation associated with peripapillary and radial zones of retinal pigment epithelial atrophy that are distributed along the retinal veins, commonly bilateral and symmetric. The diagnosis of PPRCA is based on typical and characteristic fundus appearance. <\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Vision is rarely affected and it is an incidental finding. Color vision is unaffected. Macular involvement is rare but cystoid macular edema have been reported.  <\/p>\n<p style=\"text-align: justify; font-size: 16px;\">Although the etiology of PPRCA is unknown, inflammatory and infectious causes have been reported and it is possible that it has a genetic basis.<\/p>\n<p style=\"text-align: justify; font-size: 16px;\">The differential diagnoses include chorioretinal degeneration and inflammatory diseases that cause chorioretinal atrophy.<\/p>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][vc_column width=&#8221;1\/4&#8243;][vc_images_carousel images=&#8221;113480,113484&#8243; img_size=&#8221;medium&#8221; speed=&#8221;2000&#8243; autoplay=&#8221;yes&#8221; hide_pagination_control=&#8221;yes&#8221; wrap=&#8221;yes&#8221; css=&#8221;.vc_custom_1752584802417{margin-bottom: 10px !important;}&#8221;]<div class=\"stats-block stats-left  \"><div class=\"aio-icon-left\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon square \"  style=\"color:#333333;background:#ffffff;font-size:32px;display:inline-block;\">\n\t<i class=\"Defaults-eye\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"stats-desc\" id=\"counter-responsv-wrap-5789\"><div id=\"counter_36681935306a03c7a22d6d2\" data-id=\"counter_36681935306a03c7a22d6d2\"  data-ultimate-target='#counter-responsv-wrap-5789 .stats-number'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  class=\"stats-number ult-responsive\" style=\"font-size:28px;  \" data-speed=\"3\" data-counter-value=\"1\" data-separator=\",\" data-decimal=\".\">0<\/div><div id=\"title-counter_36681935306a03c7a22d6d2\"  data-ultimate-target='#counter-responsv-wrap-5789 .stats-text'  data-responsive-json-new='{\"font-size\":\"desktop:16px;\",\"line-height\":\"\"}'  class=\"stats-text ult-responsive\" style=\"font-size:px;  font-weight:bold;\">Clinical Cases<\/div><\/div><\/div>[\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text css=&#8221;.vc_custom_1752584816546{margin-bottom: 10px !important;}&#8221;]<\/p>\n<h1><strong><span style=\"color: #5f1b52;\">Clinical Cases<\/span><\/strong><\/h1>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;1\/4&#8243;][vc_column_text css=&#8221;.vc_custom_1752584833396{margin-bottom: 0px !important;}&#8221;]<\/p>\n<h4 style=\"text-align: left;\"><a href=\"https:\/\/www.atlasrleye.com\/en\/pigmented-paravenous-retinochoroidal-atrophy\/clinical-case-1\/\">Clinical Case 1<\/a><\/h4>\n<p>[\/vc_column_text][vc_gallery type=&#8221;image_grid&#8221; images=&#8221;113480,113484&#8243; img_size=&#8221;150&#8243; css=&#8221;.vc_custom_1752584844986{margin-bottom: 10px !important;margin-left: -20px !important;}&#8221;][vc_row_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-3609\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-calendar\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-3609 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">1<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-2339\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-camera\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-2339 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">10<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][vc_column_inner width=&#8221;1\/5&#8243; offset=&#8221;vc_col-xs-1\/5&#8243;]<div class=\"aio-icon-component    style_1\"><div id=\"Info-box-wrap-6106\" class=\"aio-icon-box default-icon\" style=\"\"  ><div class=\"aio-icon-default\"><div class=\"ult-just-icon-wrapper  \"><div class=\"align-icon\" style=\"text-align:center;\">\n<div class=\"aio-icon none \"  style=\"color:#5f1b52;font-size:16px;display:inline-block;\">\n\t<i class=\"Defaults-film\"><\/i>\n<\/div><\/div><\/div><\/div><div class=\"aio-icon-header\" ><h3 class=\"aio-icon-title ult-responsive\"  data-ultimate-target='#Info-box-wrap-6106 .aio-icon-title'  data-responsive-json-new='{\"font-size\":\"\",\"line-height\":\"\"}'  style=\"color:#5f1b52;\">0<\/h3><\/div> <!-- header --><\/div> <!-- aio-icon-box --><\/div> <!-- aio-icon-component -->[\/vc_column_inner][\/vc_row_inner][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row][vc_column][vc_custom_heading text=&#8221;RETINAL DYSTROPHIES AND SYNDROMES&#8221; font_container=&#8221;tag:h5|font_size:22px|text_align:center|color:%23000000&#8243; use_theme_fonts=&#8221;yes&#8221; link=&#8221;url:https%3A%2F%2Fwww.atlasrleye.com%2Fen%2Fatlas%2F%231636632807269-1444524b-3ed4|&#8221;][vc_text_separator title=&#8221;&#8221; i_icon_fontawesome=&#8221;fas fa-eye&#8221; i_color=&#8221;custom&#8221; i_size=&#8221;lg&#8221; color=&#8221;custom&#8221; border_width=&#8221;8&#8243; css=&#8221;.vc_custom_1637080776101{margin-bottom: -5px !important;}&#8221; add_icon=&#8221;true&#8221; accent_color=&#8221;#bababa&#8221; i_custom_color=&#8221;#bababa&#8221;][vc_custom_heading source=&#8221;post_title&#8221; font_container=&#8221;tag:h1|font_size:44px|text_align:center|color:%235f1b52&#8243; use_theme_fonts=&#8221;yes&#8221;][\/vc_column][\/vc_row][vc_row][vc_column width=&#8221;3\/4&#8243;][vc_column_text css=&#8221;&#8221;] Pigmented Paravenous Retinochoroidal Atrophy (PPRCA) is a rare disorder of unknown etiology, characterized by [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"class_list":["post-113600","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/113600","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/comments?post=113600"}],"version-history":[{"count":8,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/113600\/revisions"}],"predecessor-version":[{"id":118178,"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/pages\/113600\/revisions\/118178"}],"wp:attachment":[{"href":"https:\/\/www.atlasrleye.com\/en\/wp-json\/wp\/v2\/media?parent=113600"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}